Cystic Fibrosis

Many people may know or heard of the name Boomer Esiason. Many may not have either. Mr. Esisaon was a pretty good football player. He had a great high school career, he played at the University of Maryland setting 17 school records and made a pretty solid career in the NFL; playing for such teams as Cincinnati, New York Jets, and Arizona. After his career was diminishing he went into broadcasting and still to this day is on T.V. (2010) However you would think that the way his life just kept moving forward that he was a natural and nothing in his own life could stop him. Well, nothing in HIS own life went wrong. It was the life of his first born son Gunner where things went wrong. According to Esiason.org, Boomer was at a New York Jets mini camp when his wife notified him that their son Gunner was diagnosed with Cystic Fibrosis. Their son started developing breathing and digestive problems and that’s how it came about. Boomer was devastated. According to Mahalo.com, Gunner was diagnosed at the early age of 2. (2006)
Cystic Fibrosis is not something that you can prevent my eating healthy or something that is pill treatable. Cystic Fibrosis is something that is inherited from a parent’s defective gene and its protein product (2010). It is caused by a mutation on seventh chromosome. There are many symptoms of Cystic fibrosis. Cystic Fibrosis is detected at a young age.
The first sign of Cystic Fibrosis is coughing and having problems breathing. This happens because the protein of the defective gene causes the body to produce thick, sticky mucus that clogs the lungs. When the lungs are clogged it can cause lung infection, stop natural enzymes from helping the body break down and absorb food (2010). Also air ways get blocked with the mucus.
Other symptoms of Cystic Fibrosis are that the skin becomes very salty. This is because Cystic Fibrosis causes sweat to become very salty. The increase of the salt in a person with Cystic Fibrosis causes high cases of dehydration, increased heart rate, tiredness, weakness, decreased blood pressure, heat strokes, and sometimes death. Cystic Fibrosis mostly affects the lungs and pancreas. Cystic Fibrosis can also affect the reproductive organs and the liver (2010).
Right now there is no cure for cystic fibrosis. There are many different types of remedies but there is nothing that will completely cure cystic fibrosis. The two main problems with cystic fibrosis are lung damage and digestion problems. So these are the two main things scientists try and cure. They do this by treating chest infections and prevent further damage to the lungs, and improve nutrition by adding supplements to help digestion. Many cystic fibrosis patients are in counseling to help them cope with the emotional and psychological aspects of their illness.
The best way to help digestion is to take a wide range of medicines. One major medicine you can take is pancreatican which helps with digestion of food. You can also take regular antibiotics to counter lung infection. Also there mucolytics to make your mucus less sticky which helps the lungs. You can start asthma therapy to help treat blocked airways and breathing problems. If you have diabetes you can do insulin therapy to help break down sugar properly.
One way in the future we can treat Cystic Fibrosis is by using gene therapy. Cystic Fibrosis is a genetic disease so it is something that is passed on from parent to child. So you test a person’s genes at an early enough age you could repair or replace the defective gene. As of now though gene therapy does not exist.
The only other treatment for Cystic Fibrosis is chest therapy. This is when you drain the mucus from the person’s chest. They do this so they can unobstructed the airway so the person can breath better. The doctor will do this over multiple spots over the chest. This will improve the patients overall condition.
Cystic fibrosis is an inherited disease, and unfortunately there is no cure for the disease. Despite the fact that there is no cure, there is till therapy and treatment that a person can undergo to help fight cystic fibrosis. There are specific drugs that can be taken to help clear the cystic fibrosis mucus from the airways and reduce inflammation. Postural drainage and percussion is a technique that is used to clear the airways in patients with cystic fibrosis. This technique requires the patient to sit, stand, or lie in a position that allows their chest and back to be pounded or clapped. There are several types of inhaled medications that can be used, as well. Antibiotics and other drugs can also be used to help fight cystic fibrosis, but a simple does of ibuprofen is actually proven to help control the disease. Patients should be strictly monitored if taking ibuprofen though. Therapy can help cystic fibrosis, and there is continued research in this area, but as for now, there is no cure for the disease.
Boomer Esiason has created the Boomer Esiason Foundation where all proceeds go to cystic fibrosis research. In a matter of almost two decades the foundation has brought tremendous light to all cystic fibrosis inquirers. According to the Boomer Esiason Foundation their mission is “a dynamic partnership of leaders in the medical and business communities joining with a committed core of volunteers to heighten awareness, education and the quality of life for those affected by cystic fibrosis, while providing financial support to research aimed at finding a cure.”(2009) Gunnar Esiason is now in his second semester at Boston College as a freshman; He has fought all odds.(2010) Gunnar Esiason was only expected to live until he was 14,(2006) but because of research he and 30,000 (2005) others have become fighters.


1. Pinkerton, K. (2006, November 9). Cystic Fibrosis Life Expectancy. Retrieved March 11, 2010, from http://ezinearticles.com/?Cystic-­Fibrosis-­Life-­Expectancy&id=353570
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3. Gunnar esiason. (n.d.). Retrieved from
4.http: www.cff.org

5. Cystic fibrosis foundation. (2009, October 20). Retrieved from http://www.cff.org/aboutcf/faqs/
6. Fighting cystic fibrosis. (n.d.). Retrieved from
7.Cystic Fibrosis Foundation. About Cystic Fibrosis. 2010. Retrieved from:
8.The Medical News. Cystic Fibrosis Facts. 2010. Retrieved from:
9.Teens Health. Cystic Fibrosis. 2010. Retrieved from
10. http://www.cff.org/treatments/Therapies/

Courtney Crislip’s Notes
New Pig Model of Cystic Fibrosis
Lays Groundwork for Better Understanding of Human Di

Before now, mice have been the only animal model for CF. However since mice do not exhibit typical symptoms of CF, and the lung and liver diseases found in humans, finding a better model was crucial to furthering CF research.

Lung disease in CF is caused by infection and inflammation. Which comes first remains an important question for CF researchers. At birth, researchers found no evidence of infection or inflammation in the pigs, a situation similar to newborn humans with CF.

"By tracking how the lungs of these pigs respond to challenges to their respiratory systems introduced by the environment, we hope to better understand how the complications of CF progress in children," said Michael J. Welsh, M.D., University of Iowa and the Howard Hughes Medical Institute, and senior author of the study.

(2008). New Pig Model of Cystic Fibrosis Lays Groundwork for Better
Understanding of Human Disease.
NIHNEWS. Retrieved from

Boomer Esiason mounts winning drive against Cystic Fibrosis

"Doctors sometimes think CF is asthma or allergies or a viral infection," Esiason cautions. "As parents, you're predisposed to want to think it's the least severe illness and you hope that it is. It is critically important that parents seek out well qualified doctors and hospital that know what to look for."

Esiason is not alone in that fight. Many don't even know their children could be born with CF.

"I am a big believer in genetic testing," Esiason says. "Before you have kids, I think people should consider finding out where they stand. If you're Jewish, you'd likely think about Tay-Sachs testing. If you fit into the risk group for CF, which is primarily northern European descent, why wouldn't you get tested to see if you carry the gene? It's a very easy test."

Morgan, J. (2004). Boomer Esiason mounts winning drive against Cystic Fibrosis.
USA Today. Retrieved from

Gene Tests Appear to Reduce Levels of some Inherited

Genetic testing pushes hot-button issues: abortion, embryo destruction and worries about eugenics — selective breeding to rid a population of unwanted traits. Yet it is touching a growing number of people

Although genetic testing can raise moral dilemmas, at least one conservative religious group — Orthodox Jews — has found ethically acceptable ways to use it to lessen diseases that have plagued its populations.

Lots of eyes are on cystic fibrosis, a disease that causes sticky mucus buildup in the lungs, digestive problems and death in young adulthood. More than 10 million Americans — one in 25 to 29 whites, who are more at risk for it than blacks — carry a gene mutation for it. In 2001, the American College of Obstetricians and Gynecologists and other groups recommended that white pregnant women be offered testing for mutations. Tests on partners and fetuses often followed, and an unknown number of abortions.

MARCHIONE, M. ( 2010). Gene Tests Appear to Reduce Levels of some Inherited
The Washington Examiner. Retrieved from

Tim Sutcliffe's notes

1. Utahns with cystic fibrosis face challenges, but strive to live 'every day to its fullest.'

-Some parents are opting not to have their children if they are going to have cystic fibrosis.
-There is no cure for cystic fibrosis, but medicines can be given to help patients absorb nutrients.
-10 million Americans are thought to have some form of mutation that could lead to the disease cystic fibrosis.

Source: Heather, M. (2010, Feb 11). Utahns with cystic fibrosis face challenges, but
strive to live 'every day to its fullest.'
Salt Lake Tribune. Retrieved from

2. The Voices of Cystic Fibrosis

CF is an inherited disease that affects about 30,000 children and adults in the USA.
-Patients with CF have a life expectancy of around 30-40 years old, much higher than it was in previous decades.
-One person dies every day from cystic fibrosis.

Source: Parker-Pope, T. (2009, June 11). The Voices of Cystic Fibrosis.
New York Times.
Retrieved from http://well.blogs.nytimes.com/2009/06/11/the-voices-of-cystic-

3. Cystic Fibrosis

-Diabetes, liver failure, and infertility can be symptoms of CF
-The cause of cystic fibrosis is due to a faulty gene on chromosome 7, which controls the salt and water movements in the body.
-High energy foods, enzyme supplements, and vitamin supplements are the only things that a person with CF can do to get the nutrients they need.

Source: Hicks, R. and McNair, T. (2010, Feb 17). Cystic Fibrosis.
BBC Health. Retrieved
from http://www.bbc.co.uk/health/conditions/cystic1.shtml

Matt Parson's notes

1. -pressured whey protein could have huge benefits for CF
-this is because whey protein helps nutritional and reduces inflamatory
-children should consume 20 to 40 grams of whey protein a day.

Hutchinson, Barbara, Greider, Antoinette, (Jr.), Edgar, Service, American, Elsevier, Elsevier, Glose, Mary, & Hedblad, Alan. (2004).
Gale directory of publications and broadcast media. Gale / Cengage Learning.

2.- a chronic, life-threatening, life-limiting disease that demands a relentless regime of daily treatment
-people with CF pursue a future that is threatened and continually redefined
-care can be delivered from an empathetic bearing toward those for whom it is not so much a bothersome routine

York, City, (Firm), EBSCO, Publications, Sage, inc, inc, service), Sage, Illumina, CSA, Online, OCLC, Hall, Richard, Theater, Temple, Online, OCLC, University), Institute, Nobari, Nuchine, Publications, Sage, & inc, inc. (2005).
Gale directory of publications & broadcast media 140. Gale Cengage.

3. Cystic Fibrosis is one of the most common life threating inheirted disease.
-There are 1,000 CF mutations
-DF508 is the most common, with a frequency varying between 50% and 70%

Gorton, Lo, Dept, Great, Fisheries, Great, Agriculture, Great, Food, Fisheries, Robinson, Edgar, Office, United, Division, United, State, Michigan., Administration, Michigan., Budget, Michigan., Bureau, Michigan., Trojanowicz, Marek, Agency, International, Salamon, Maciej, & Fisheries, Great. (1977).
fisheries statistical tables//. Intl Atomic Energy Agency
external image CFS-CureCysticFibrosisMagnet.jpg

CF Taskstream website

Ashley Dick

Nation Human Genome Research Institute.

Fact One: The gene for cystic fibrosis was discovered in 1989. The CFTR gene (the mutated gene-Cystic Fibrosis Transmembrane Regulator)

Fact Two: Symptoms of cystic fibrosis are salty-tasting skin, an ongoing cough, eat a lot but have a hard time keeping on weight

Fact Three: Genetic research may lead to new drugs that are made from bacteria that may be able to help treat CF.

Fact Four: 1 in 31 people in the United States are carriers of the mutated CF gene

Fact Five: CF cause a heavy mucus that makes it hard for a person with CF to breath

Nation Human Genome Research Institute. National Institute of Health. December 21, 2009.

Day-to-Day School and CF.

Fact One: A child with CF cannot be denied day care services
-The ADA- the Americans with Disabilities Act – says that day care cannot refuse a CF child.

Fact Two: IEP are given to students with CF.
-there has to be adjusted schedules so that the student to take medication and do treatments, sometimes even therapy

Fact Three: Teachers have to be very flexible with a CF child because they may have to leave the class multiple times.
Fact Four: If child with CF is denied an IEP plan than they can request a 504 plan

Fact Five: A child that has CF is labeled as a disability

Day-to-Day School and CF. Cystic Fibrosis Foundation. 2004. Pgs 1-7 http://www.cff.org/UploadedFiles/LivingWithCF/AtSchool/SchoolAndCF/Day%20to%20Day%20--%20School%20and%20CF%2008-05.pdf

About Cystic Fibrosis.

Fact One : Over 70% of CF patients are diagnosed by the age of two.

Fact Two: Median age of survival for a person with CF is more than 37

Fact Three: A person with CF has a very high chance of lung infection

Fact Four: CF patient have a very hard time using the bathroom and can be hospitalized for help bowel movement.

Fact Five: 70,000 people worldwide have CF

About Cystic Fibrosis. Cystic Fibrosis Foundation. 2010. http://www.cff.org/great_strides/cffactsheet/